Renal cell carcinoma is the most common renal malignancy in adults and extremely rare in children. It may present with hematuria, flank pain and palpable mass. Treatment protocols for renal cell carcinoma in children have not yet been well-defined due to the rarity of the desease, however surgery remains the mainstay treatment for tumors that are resectable. Presented here is a case of a 1 year old female presenting with left hemiabdominal mass, who underwent transabdominal left radical nephrectomy. Histopathology showed a papillary renal cell carcinoma type 1, with positive immunohistochemical stains for Vimentin, CK7 and AMACR.