Renal Rhabdomyosarcoma, Pleomorhic Variant in a 61-year old Male

Abstract

Renal rhabdhomyosarcoma is a rare subtype of renal sarcoma in adults that arise from skeletal muscle progenitor cells. Primary rhabdomyosarcomas are usually seen in the pediatric population and extremely rare in adults. This is a case of 61 year old, male who presented with a 3 week history of a palpable left upper quadrant mass accompanied by early satiety, anorexia, weight loss and dysuria. Ultrasound of whole abdomen revealed a hydronephrotic left kidney with no noted lithiasis and unremarkable right kidney. CT scan of the abdomen was chronic cystic pyelonephritis vs renal neoplasm, left paraaortic or perirenal lymphadenopathy suggestive of regional node metastasis. The case was diagnosed as Left Renal New Growth with consideration of Renal Cell Carcinoma (T2bN1M0). Hence the patient underwent cytoreductive nephrectomy. The histopathologic report revealed pleomorphic rhabdomyosarcoma. Literature review of renal rhabdomyosarcoma regarding symptomatology, diagnostic modality, treatment standard, adjuvant therapy and prognosis was done.