TRES-ticles: A Rare Case of a Discontinous Type of Splenogonadal Fusion Presenting as Polyorchidism

Abstract

Polyorchidism is a very rare congenital anomaly, which is defined as having more than 2 testicles in a human male. To date, there are only a number of cases reported worldwide and most of them are published as case reports. Most cases of polyorchidism are associated with other male genitourinary anomalies such as varicoceles, hydroceles, inguinal hernias, and testicular malignancies. Even much more rarer are accessory spleens located intrascrotally, with only a handful of case reports in the last 80 years. Reported here is a case of a 33-year old male presenting with symptoms of intermittent scrotal pain for 2 years and extratesticular mass on ultrasound. Surgical management for this patient was done, removing one of the accessory testicles. Histopathology showed as an accessory spleen. Since this is a rare occurrence, the authors aimed to present splenunculus as a differential for patients with polyorchidism.